Heterotaxy syndrome is a rare disease, and asplenia with congenital heart disease syndrome, also known as Ivemark syndrome, is a special form of heterotaxy syndrome. These patients usually have severe cardiovascular malformations and a poor prognosis. Their surgical outcomes are rarely satisfactory. We report the case of a 14-year-old patient who underwent successful corrective surgery treatment.

中文翻译：

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14 岁先天性心脏病综合征无脾患者双心室修复成功

异位综合征是一种罕见病，先天性心脏病无脾综合征又称Ivemark综合征，是异位综合征的一种特殊形式。这些患者通常有严重的心血管畸形和不良预后。他们的手术结果很少令人满意。我们报告了一名成功接受矫正手术治疗的 14 岁患者的病例。