Congenital proximal radioulnar synostosis (CPRUS) is a rare anomaly which is caused by abnormal fusion of the proximal radius and ulna during development. This is due to the failure of embryological separation, resulting in the fixed position of the forearm, from mild to severe pronation.1 Mild deformity leads to slight disability because the shoulder and wrist can effectively compensate.2 Patients with bilateral cases and/or pronation deformity of >60° may be severely limited in daily activities.3 4 Most surgeons recommend surgical intervention when the loss of forearm rotation exceeds 60°, particularly when the forearm is fixed in pronation.5 Even when restoring a complete range of motion (ROM) is impossible, surgical management of congenital radioulnar synostosis enhances limb function.5 6 Currently, the most common treatment for CPRUS is rotational osteotomy of the proximal ulna and distal radius, either single-stage rotational correction or two-stage rotational correction. The aim of this study was to analyze the clinical outcomes of two-stage rotational correction after osteotomy of the proximal ulna and distal radius in patients with CPRUS who had fixed pronation deformity. We selected 17 children (26 forearms) with CPRUS who were consecutively treated in the Department of Orthopedics, the Children Hospital …

中文翻译：

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两期双节段旋转截骨术治疗先天性近端尺桡骨关节早闭的疗效

先天性近端尺桡关节早闭（CPRUS）是一种罕见的畸形，由发育过程中桡骨近端和尺骨近端的异常融合引起。这是由于胚胎分离失败，导致前臂固定位置，从轻度旋前到重度旋前。1 轻度畸形导致轻微残疾，因为肩部和腕部可以有效代偿。2 双侧病例和/或旋前患者>60° 的畸形在日常活动中可能会受到严重限制。3 4 大多数外科医生建议在前臂旋转超过 60° 时进行手术干预，特别是当前臂固定在旋前时。5 即使在恢复完整的运动范围（ROM ) 是不可能的，先天性尺桡关节早闭的手术治疗可增强肢体功能。5 6 目前，CPRUS 最常见的治疗方法是近端尺骨和远端桡骨的旋转截骨术，可以是单级旋转矫正或两级旋转矫正。本研究的目的是分析固定旋前畸形的 CPRUS 患者尺骨近端和桡骨远端截骨术后两阶段旋转矫正的临床结果。我们选择了 17 名 CPRUS 儿童（26 条前臂），他们在儿童医院骨科连续接受治疗…… 本研究的目的是分析固定旋前畸形的 CPRUS 患者尺骨近端和桡骨远端截骨术后两阶段旋转矫正的临床结果。我们选择了 17 名 CPRUS 儿童（26 条前臂），他们在儿童医院骨科连续接受治疗…… 本研究的目的是分析固定旋前畸形的 CPRUS 患者尺骨近端和桡骨远端截骨术后两阶段旋转矫正的临床结果。我们选择了 17 名 CPRUS 儿童（26 条前臂），他们在儿童医院骨科连续接受治疗……