Primary immunodeficiency diseases (PIDs), also called inborn errors of immunity (IEI), are genetic disorders characterized by increased susceptibility to infection and/or aberrant regulation of immunological pathways. This review summarizes and highlights the new IEI disorders in the International Union of Immunological Societies (IUIS) 2022 report and current trends among new PIDs.

中文翻译：

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2023 年新原发性免疫缺陷病更新。

原发性免疫缺陷病 (PID)，也称为先天性免疫缺陷 (IEI)，是一种遗传性疾病，其特征是感染易感性增加和/或免疫途径调节异常。本综述总结并强调了国际免疫学会联盟 (IUIS) 2022 年报告中的新 IEI 疾病以及新 PID 的当前趋势。