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Inflammatory myofibroblastic tumor in pediatric patients: challenges in diagnosis, multidisciplinary management, and surgical strategies
Egyptian Pediatric Association Gazette Pub Date : 2024-03-29 , DOI: 10.1186/s43054-024-00269-z
Izchel Valdez García , Alejandro Solano Gutierrez , Sofia Brenes Guzmán , Brenda Aguilar Viveros

Inflammatory myofibroblastic tumor is a rare yet profoundly impactful condition, particularly within the pediatric population. This case report illuminates the intricate challenges of diagnosing and managing inflammatory myofibroblastic tumors in children, underscoring the importance of interdisciplinary collaboration in formulating effective treatment strategies. Notably, the choice of surgical approach holds a paramount influence on the risk of recurrence and metastasis, with wide resection with bronchotomy, lobectomy, and pneumonectomy demonstrating significantly diminished recurrence rates compared to wedge resection in bronchoscopic removal. We present the case of a 3-year-old girl with a progressive, nonproductive cough, occasionally accompanied by episodes of hemoptysis and pneumonia for a year, secondary to an inflammatory myofibroblastic tumor that was removed by bronchotomy with excellent results. Given the extraordinary rarity of this disease in pediatric patients, ongoing research endeavors and the accumulation of collective expertise are paramount.

中文翻译:

儿科患者炎症性肌纤维母细胞肿瘤:诊断、多学科管理和手术策略方面的挑战

炎性肌纤维母细胞肿瘤是一种罕见但影响深远的疾病,特别是在儿科人群中。本病例报告阐明了诊断和治疗儿童炎症性肌纤维母细胞肿瘤的复杂挑战,强调了跨学科合作在制定有效治疗策略方面的重要性。值得注意的是,手术方法的选择对复发和转移的风险具有至关重要的影响,与支气管镜切除中的楔形切除术相比,支气管切开术、肺叶切除术和全肺切除术的广泛切除表明复发率显着降低。我们介绍了一名 3 岁女孩的病例,她患有进行性、干咳,偶尔伴有咯血和肺炎,持续一年,继发于炎症性肌纤维母细胞瘤,通过支气管切开术切除,效果良好。鉴于这种疾病在儿科患者中极其罕见,持续的研究努力和集体专业知识的积累至关重要。
更新日期:2024-03-29
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