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A Case of Ventricular Fibrillation in Masked Long-QT Syndrome Coexisting with Coronary Vasospasm
International Heart Journal ( IF 1.5 ) Pub Date : 2024-03-30 , DOI: 10.1536/ihj.23-397
Atsumasa Kurozumi 1 , Yoshinari Enomoto 1 , Hisao Hara 1 , Norihiro Kato 1, 2 , Yukio Hiroi 1
Affiliation  

Although long-QT syndrome (LQTS) with a normal range QT interval at rest leads to fatal ventricular arrhythmias, it is difficult to diagnose. In this article, we present a rare case of a patient who suffered a cardiac arrest and was recently diagnosed with LQTS and coronary vasospasm. A 62-year-old man with no syncopal episodes had a cardiopulmonary arrest while running. During coronary angiography, vasospasm was induced and we prescribed coronary vasodilators, including calcium channel blockers. An exercise stress test was performed to evaluate the effect of medications and accidentally unveiled exercise-induced QT prolongation. He was diagnosed with LQTS based on diagnostic criteria. Pharmacotherapy and an implantable cardioverter defibrillator were used for his medical management. It is extremely rare for LQTS and coronary vasospasm to coexist. In cases of exercise-induced arrhythmic events, the exercise stress test might be helpful to diagnose underlying disease.



中文翻译:

蒙蔽长QT综合征心室颤动合并冠状动脉痉挛一例

尽管静息时 QT 间期正常范围的长 QT 综合征 (LQTS) 会导致致命的室性心律失常,但诊断起来很困难。在本文中,我们介绍了一名罕见的心脏骤停患者,最近被诊断患有 LQTS 和冠状血管痉挛。一名没有晕厥发作的 62 岁男子在跑步时出现心肺骤停。在冠状动脉造影期间,诱发血管痉挛,我们开了冠状血管扩张剂,包括钙通道阻滞剂。进行运动压力测试来评估药物的效果,并意外地发现了运动引起的 QT 延长。根据诊断标准,他被诊断为 LQTS。药物治疗和植入式心脏复律除颤器用于他的医疗治疗。 LQTS 和冠状血管痉挛同时存在的情况极为罕见。在运动引起的心律失常事件的情况下,运动负荷测试可能有助于诊断潜在疾病。

更新日期:2024-03-31
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