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Multimodality Imaging Approach Evaluation of the Congenital Pericardial Defect: a Contemporary Review

  • Pericardial Disease (AL Klein and CL Jellis, Section Editors)
  • Published:
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Abstract

Purpose of Review

This review presents the etiology, clinical manifestations, diagnostic approach, and treatment of congenital pericardial defects. It also highlights the critical role of echocardiography, cardiac computed tomography (CCT), and cardiac magnetic resonance (CMR) in the diagnosis and management approach.

Recent Findings

Congenital pericardial defects are rare. Although most cases are found incidentally, some cases could potentially be associated with serious outcomes including sudden cardiac death. The diagnosis is often challenging due to non-specific clinical manifestations and electrocardiogram findings.

Summary

Echocardiography is the first-line imaging investigation for the evaluation of this condition. Advanced cardiac imaging modalities, including CCT and CMR, play important adjuvant roles in establishing the diagnosis and assists with prognostication.

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Authors and Affiliations

  1. Robert and Suzanne Tomsich Department of Cardiovascular Medicine, Sydnell and Arnold Family Heart, Vascular, and Thoracic Institute, Cleveland Clinic Foundation, Cleveland, OH, 44195, USA

    Mohamed Khayata & Alice A. Haouzi

  2. Section of Cardiovascular Medicine, Cleveland Clinic Florida, Weston, FL, 33331, USA

    Craig R. Asher

  3. Section of Cardiovascular Imaging, Robert and Suzanne Tomsich Department of Cardiovascular Medicine, Sydnell and Arnold Family Heart, Vascular, and Thoracic Institute, Cleveland Clinic Foundation, Cleveland, OH, 44195, USA

    Bo Xu

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  1. Mohamed Khayata
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  2. Alice A. Haouzi
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  4. Bo Xu
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Correspondence to Bo Xu.

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Khayata, M., Haouzi, A.A., Asher, C.R. et al. Multimodality Imaging Approach Evaluation of the Congenital Pericardial Defect: a Contemporary Review. Curr Cardiol Rep 25, 1715–1724 (2023). https://doi.org/10.1007/s11886-023-02004-3

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