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Behavioural interventions to increase adherence to palivizumab prophylaxis in children with CHD Cardiol. Young (IF 1.0) Pub Date : 2024-04-26 Elif Erolu, Özgür Kıbrıs, Yasemin Tosun, Ayse Yildirim, Ozge Pamukcu, Evic Zeynep Basar, Kadir Babaoglu, Serdar Epcacan, Yasemin Donmez, Dilek Giray, Pınar Dervisoglu, Onur Tascı
Objectives: Adherence to palivizumab prophylaxis programmes is crucial to protect infants with CHD against respiratory syncytial virus infections. We analysed the effectiveness of two nudge interventions in increasing adherence.Methods: Our study included 229 infants, and their caregivers, from five centers in Turkey in the 2020–2021 respiratory syncytial virus season. We randomly allocated caregivers
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Cardiac resternotomy after cardiac surgery in kids: CRACK the chest Cardiol. Young (IF 1.0) Pub Date : 2024-04-25 Jui Shah, Ashley Sefton, John Dentel, Bradley Tilford, Katherine Cashen
Objective: Emergent resuscitation of postoperative paediatric cardiac surgical patients requires specialised skills and multidisciplinary teamwork. Bedside resternotomy is a rare but life-saving procedure and few studies focus on ways to prepare providers and improve performance. We created a multidisciplinary educational intervention that addressed teamwork and technical skills. We aimed to evaluate
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Successful oral midodrine therapy for treatment of refractory postoperative chylothorax in an infant Cardiol. Young (IF 1.0) Pub Date : 2024-04-25 Shunsuke Nukaga, Fujito Numano, Akihiko Saitoh
Refractory chylothorax, a postoperative complication of CHD, is difficult to manage and sometimes fatal. Herein, we report the case of a 10-month-old infant with 22-mosaic trisomy and a coarctation complex, who developed refractory chylothorax after cardiac repairs and was successfully treated with midodrine, an oral alpha-1-adrenoreceptor agonist. Midodrine may be used as adjunctive therapy for postoperative
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Case report: Prinzmetal angina in adolescent Cardiol. Young (IF 1.0) Pub Date : 2024-04-24 Anisa Rahmadhany, Birry Karim, Mohamad Yanuar Amal
Prinzmetal angina is a rare condition more likely to be reported in adults. Vasospasm is by far notable for causing this condition. We present a case of Prinzmetal angina in a 17-year-old male who experienced unexplained resting chest pain for 2 days.
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Prognosis and clinical management of asymptomatic family members with RYR2-mediated catecholaminergic polymorphic ventricular tachycardia: a review Cardiol. Young (IF 1.0) Pub Date : 2024-04-24 Puck J. Peltenburg, Harry Gibson, Arthur A. M. Wilde, Christian van der Werf, Sally-Ann B. Clur, Nico A. Blom
Despite its low prevalence, the potential diagnosis of catecholaminergic polymorphic ventricular tachycardia (CPVT) should be at the forefront of a paediatric cardiologists mind in children with syncope during exercise or emotions. Over the years, the number of children with a genetic diagnosis of CPVT due to a (likely) pathogenic RYR2 variant early in life and prior to the onset of symptoms has increased
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Racial, ethnic, and socio-economic disparities in neonatal ICU admissions among neonates born with cyanotic CHD in the United States, 2009–2018 Cardiol. Young (IF 1.0) Pub Date : 2024-04-24 Kriyana P. Reddy, Avital B. Ludomirsky, Andrea L. Jones, Rachel J. Shustak, Jennifer A. Faerber, Maryam Y. Naim, Keila N. Lopez, Laura M. Mercer-Rosa
Introduction: Disparities in CHD outcomes exist across the lifespan. However, less is known about disparities for patients with CHD admitted to neonatal ICU. We sought to identify sociodemographic disparities in neonatal ICU admissions among neonates born with cyanotic CHD. Materials & Methods: Annual natality files from the US National Center for Health Statistics for years 2009–2018 were obtained
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Paediatric resident identification of cardiac emergencies Cardiol. Young (IF 1.0) Pub Date : 2024-04-22 Brittney K. Hills, Dana B. Gal, Matthew Zackoff, Brenda Williams, Elisa Marcuccio, Melissa Klein, Ndidi Unaka
Objectives: Critical CHD is associated with morbidity and mortality, worsened by delayed diagnosis. Paediatric residents are front-line clinicians, yet identification of congenital CHD remains challenging. Current exposure to cardiology is limited in paediatric resident education. We evaluated the impact of rapid cycle deliberate practice simulation on paediatric residents’ skills, knowledge, and perceived
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Successful ablation of premature ventricular contractions originating from the posterior-superior process of the left ventricle approaching from the right atrium in a 13-year-old male Cardiol. Young (IF 1.0) Pub Date : 2024-04-22 Ryo Nakagawa, Yoko Yoshida, Tsugutoshi Suzuki
This is a case of a 13-year-old male with frequent premature ventricular contractions with QRS configurations of the left superior axis and left bundle branch block, which originated from the posterior–superior process of the left ventricle. Premature ventricular contractions were successfully eliminated by delivering radiofrequency energy to the inferior wall of the right atrium without causing either
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Predictors of psychosocial adaptation in children with CHD Cardiol. Young (IF 1.0) Pub Date : 2024-04-18 Jessica L. Metelski, Kiona Y. Allen, L. Barrera, M. Heffernan, Clayton D. Hinkle, Pooja Parikh, Carolyn C. Foster
Survival of CHD has significantly improved, but children with CHD remain susceptible to neurodevelopmental and psychosocial impairments. Our goal was to investigate the association between socio-demographic factors and psychosocial adaptation for future intervention. A retrospective cross-sectional study of an independent children’s hospital’s records was conducted. Psychosocial adaptation was measured
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Long-term outcomes after the arterial switch operation Cardiol. Young (IF 1.0) Pub Date : 2024-04-17 Zhangwei Wang, Ma Kai, Shoujun Li
Objectives: The aims of this study were to evaluate the 16-year experience with arterial switch operation at Beijing Children’s Hospital and to determine early and late mortality and late morbidity, to explore risk factors for late complications and reintervention, and finally to evaluate whether the neoaortic sinotubular junction reconstruction technique reduces late complications of arterial switch
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The use of ketorolac may reduce opioid exposure in infants less than 6 months of age undergoing congenital heart surgery Cardiol. Young (IF 1.0) Pub Date : 2024-04-17 Janae Townsend, Hania Zaki, Rohali Keesari, Kevin Maher, Susan Hupp, Joshua W. Branstetter
Objectives: Pain management for infants undergoing cardiothoracic surgery primarily utilises opioid analgesics. There is a paucity of data available for the use of non-steroidal anti-inflammatory medications such as ketorolac in this patient population. Materials and Methods: This retrospective study evaluated patients between 30 days and 6 months undergoing cardiothoracic surgery. The primary endpoint
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An unusual form of “haemodynamic vise” in supra cardiac totally anomalous pulmonary venous drainage Cardiol. Young (IF 1.0) Pub Date : 2024-04-16 Mani Ram Krishna, Vijaykumar Raju, Robert H. Anderson
We report an unusual variant of obstructed supra cardiac anomalous pulmonary venous drainage where the vertical vein is obstructed by a vice formed between the persistent arterial duct and the left pulmonary artery.
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Developing the WE BEAT Well-Being Education Programme to foster resilience and build connection in paediatric heart disease Cardiol. Young (IF 1.0) Pub Date : 2024-04-16 Melissa K. Cousino, Catherine R. Dusing, Kelly E. Rea, Thomas Glenn, Blake Armstrong, Andrea S. Les, Jesse E. Hansen, Sara K. Pasquali, Kurt R. Schumacher
Background: The study of psychological well-being and related resilient outcomes is of increasing focus in cardiovascular research. Despite the critical importance of psychological well-being and related resilient outcomes in promoting optimal cardiac health, there have been very few psychological interventions directed towards children with heart disease. This paper describes the development and theoretical
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A successful surgical management for a thrombosed giant left coronary aneurysm with right ventricular fistula in a young patient Cardiol. Young (IF 1.0) Pub Date : 2024-04-15 Yunyi Lu, Jing Wang, Liheng Ma
Giant coronary aneurysm with ventricular fistula is rare. Due to the limited data from randomised clinical trials, therapeutic strategies for coronary aneurysms predominantly rely on on case series and anecdotal evidences. Reporting cases that provide practical experience in managing these aneurysms is therefore crucial. In this article, we report a rare case of a successful surgical management for
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Transcatheter knocking of a stuck mechanical tricuspid valve Cardiol. Young (IF 1.0) Pub Date : 2024-04-15 Christopher Herron, David Morales, Shabana Shahanavaz
Immobilisation of mechanical valve leaflets can be a life-threatening complication. In the acute setting, medical therapy can be attempted but is not always successful. We present the first described case of a patient with a mechanical tricuspid valve with recurrent leaflet immobilisation that was able to be mobilised using a transcatheter knocking technique.
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Cardiology across continents: an interactive, case-based learning series Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Daniel Peck, Ashley Neal, Andrew Redington, Jeffrey P. Jacobs, Scott Wirth, Katie Brandewie, Patricia Bastero, Justin T. Tretter, Raman Krishna Kumar
Heart University [https://www.heartuniversity.org/] is a free educational website providing structured training curricula with knowledge-based testing and access to webinars and conference recordings for practicing and in-training providers of paediatric and congenital cardiac care. To date, there are over 15,000 registered website users from over 140 countries on Heart University, with over 2,000
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Differences in gross motor and fine motor outcomes for toddlers after early complex cardiac surgery Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Charlene M.T. Robertson, Sara Khademioureh, Irina A. Dinu, Julie A. Sorenson, Ari R. Joffe, for the Complex Pediatric Therapies Follow-up Program
Objectives: To determine whether gross motor scores of toddlers after complex cardiac surgery were different from fine motor scores and were adequately represented by motor composite scores and, whether acute care predictors and chronic childhood health markers of gross motor scores differed from those of fine motor.Methods: This prospective inception-cohort outcomes study included 171 toddlers after
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Factors that mediate change in creatinine and acute kidney injury after the Norwood operation: insights from high-fidelity haemodynamic monitoring data Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Rohit S. Loomba, Sheena Mansukhani, Joshua Wong
Background: Acute kidney injury is a common postoperative complication of paediatric cardiac surgery associated with increased morbidity and mortality. The purpose of this study is to characterise associations between haemodynamic parameters, clinical parameters, and medical interventions, on acute kidney injury.Methods: Nine patients with univentricular physiology undergoing the Norwood procedure
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Genetic dilated cardiomyopathy with inflammation in an infant that responded to immunosuppressive therapy evaluated using cardiovascular magnetic resonance Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Hiromitsu Shirozu, Yuichi Ishikawa, Nobuhiko Kan
Cardiovascular magnetic resonance T1 and T2 mapping reflects inflammation, fibrosis, and myocardial oedema. However, its application in infants remains uncertain. Herein, we report a three-month-old boy with dilated cardiomyopathy successfully treated with steroids. Cardiovascular magnetic resonance was useful for diagnosis based on the elevated native T1, T2, and extracellular volume and evaluation
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Intravenous iron infusion ameliorates anaemia and protein-losing enteropathy in patients after Fontan surgery: case series Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Mio Kairiku, Hisaaki Aoki
Protein-losing enteropathy is a severe complication of Fontan surgery and is associated with anaemia. Few studies have reported on the efficacy of an intravenous iron infusion for treating protein-losing enteropathy and low albuminemia after Fontan surgery. Herein, we present two cases of female patients who suffered from protein-losing enteropathy and low albuminemia following Fontan surgery, both
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Cardiac MRI evaluation of aortic biophysical properties in paediatric Turner syndrome Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Somjate Suntratonpipat, Kiera Pajunen, Elizabeth Rosolowsky, Carolina A. Escudero, Rose Girgis, Richard B. Thompson, Joseph J. Pagano, Edythe B. Tham
Background: Aortopathy in Turner syndrome is associated with aortic dilation, and the risk of dissection is increased when the aortic size index is ≥ 2–2.5 cm/m2. We evaluated the aortic biophysical properties in paediatric Turner syndrome using cardiac MRI to determine their relationship to aortic size index. Methods: Turner syndrome patients underwent cardiac MRI to evaluate ventricular function
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Effectiveness of pulmonary valve-sparing strategy for transatrial-transpulmonary repair of tetralogy of Fallot: a single institution experience Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Dien T. Minh, Uoc N. Huu, Bao L. Tuan, Mai N. Tuan, Duyen M. Dinh, Vinh T. Quang, Quang Le Hong, James St. Louis, Truong N. Ly Thinh
Objective: We report the midterm results of our strategy utilizing transatrial-transpulmonary repair for tetralogy of Fallot at a single institution in a low-middle income country. Methods: Medical records were retrospectively reviewed for 532 consecutive patients who underwent definitive repair of tetralogy of Fallot at our institution from 2010 to 2020. Results: The median age and weight of patients
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Internal thoracic artery as a growing conduit for pulmonary shunt Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Takako Nishino, Makoto Ando, Shinya Yokoyama
Studies suggest the internal thoracic artery as a shunt option due to its growth potential. However, long-term data are lacking. Here, a patient with a failing single ventricle shunt had an enlarged internal thoracic artery. We followed the patient for 12 years after converting this artery into a Blalock–Taussig shunt, analysing its growth to assess its effectiveness
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A multi-centre randomised control trial of directly observed therapy to promote medication adherence in paediatric heart transplant recipients Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Michael O. Killian, Sonnie Mayewski, Dipankar Gupta
Medication non-adherence remains a significant challenge for adolescent heart transplant recipients. Building on the success of a pilot intervention study, herein we describe the protocol for a follow-up randomised control trial using mobile video directly observed therapy, featuring several innovations, to promote medication adherence in a multi-centre sample of adolescent heart transplant patients
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Pulmonary embolism from right ventricular myxoma in a child with undiagnosed Carney complex Cardiol. Young (IF 1.0) Pub Date : 2024-04-12 Christopher A. Atkins, Katherine Cashen, Kimberly Jackson, Ziv Beckerman, Jennifer I. Sherwin
Pediatric pulmonary embolism occurs in 8.6−57 per 100,000 hospitalised children. We report a novel case of bilateral pulmonary emboli in a child presenting with dyspnoea who was found to have large right ventricular myxoma and subsequent diagnosis of Carney complex. After resection of the right ventricular myxoma and bilateral pulmonary embolectomy, she had a full recovery and an excellent outcome
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Immune control in Kawasaki disease knowledge mapping: a bibliometric analysis Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Lu Zhang, Lifeng Shi, Ruijie Zhang, Xinao Lin, Yunlei Bao, Feng Jiang, Chuyan Wu, Jimei Wang
Background: Kawasaki disease is a systemic vascular disease with an unclear pathophysiology that primarily affects children under the age of five. Research on immune control in Kawasaki disease has been gaining attention. This study aims to apply a bibliometric analysis to examine the present and future directions of immune control in Kawasaki disease. Methods: By utilizing the themes “Kawasaki disease
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Impact of right ventriculotomy on cardiac function after pulmonary valve sparing repair of tetralogy of Fallot and double outlet right ventricle with pulmonary stenosis Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Khunthorn Kadeetham, Piya Samankatiwat
Objectives: Pulmonary valve-sparing repair of tetralogy of Fallot and double outlet right ventricle with pulmonary stenosis has the advantage of reduced incidence of late pulmonary valve regurgitation and better-preserved cardiac function. However, a right ventriculotomy is sometimes necessary in order to adequately relieve subvalvular pulmonary stenosis. We aimed to compare postoperative cardiac function
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Innovation in surgical treatment of hypertrophic obstructive cardiomyopathy in children Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Zhangwei Wang, Kai Ma, Yaobin Zhu, Shoujun Li
Hypertrophic cardiomyopathy is the second most common cardiomyopathy affecting children and adolescents and is the main cause of sudden death of young athletes. The natural prognosis of children with severe hypertrophic obstructive cardiomyopathy is not optimistic, and it is not uncommon for children with hypertrophic obstructive cardiomyopathy who do not respond to medication. Surgical treatment is
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Predictive value of red cell distribution width in children with pulmonary arterial hypertension associated with CHD Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Doaa El Amrousy, Mona Hashem, Hassnaa Hassan, Hossam Hodeib, Rehab Elmeazawy
Background: Pulmonary arterial hypertension, a common consequence of untreated CHD, is associated with a significant morbidity and mortality. Recent researches have demonstrated that patients with clinically severe cardiovascular illnesses, including pulmonary hypertension, have a greater mortality risk when their red cell distribution width is high. This work aimed to assess the predictive value of
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Safety, timing, and outcomes of early post-operative cardiac catheterisation following congenital heart surgery Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Karoline Krzywda, Jeremy T. Affolter, Darcie M. Al-Hassan, William J. Gibson, Ryan A. Romans, Hung-Wen Yeh, Kelly S. Tieves
Objective: The safety of early post-operative cardiac catheterisation has been described following congenital heart surgery. Optimal timing of early post-operative cardiac catheterisation remains uncertain. The aim of this study was to describe the safety of early post-operative cardiac catheterisation and its impact on cardiac ICU and hospital length of stay, duration of mechanical ventilation, and
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Transcatheter patent ductus arteriosus closure in premature infants requiring high-frequency ventilation Cardiol. Young (IF 1.0) Pub Date : 2024-04-11 Stephen T. Dalby, Sherry E. Courtney, Megha Sharma, Michael J. Angtuaco
Transcatheter closure has become a common treatment method for patent ductus arteriosus in premature infants at many centres; however, many remain uncertain about the ability to perform the procedure in the catheterisation laboratory for infants requiring high-frequency ventilation. This study presents our centre’s experience following the implementation of neonatal ventilatory guidelines, which resulted
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Long-term global longitudinal strain abnormalities in paediatric patients after multisystem inflammatory syndrome in children correlate with cardiac troponin T: a single-centre cohort study Cardiol. Young (IF 1.0) Pub Date : 2024-04-08 Stejara A. Netea, Giske Biesbroek, Maarten Groenink, R.N. (Nils) Planken, Robbert J. de Winter, Kawasaki Study Group, Nico A. Blom, Taco W. Kuijpers, Irene M. Kuipers
Background: Multisystem inflammatory syndrome in children is an inflammatory syndrome related to severe acute respiratory syndrome coronavirus 2 with a high risk of cardiovascular complications (vasoplegia, cardiac shock). We investigated the cardiac outcomes in multisystem inflammatory syndrome in children, focusing on the identification of predictors for late cardiac function impairment.Methods:
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Evaluation of cardiac functions in children with familial Mediterranean fever Cardiol. Young (IF 1.0) Pub Date : 2024-04-08 Sema Yildirim Arslan, Dolunay Gurses, Selcuk Yuksel
Objectives: Familial Mediterranean fever is an autosomal recessive autoinflammatory inherited disease. We aimed to evaluate cardiac involvement in children with familial Mediterranean fever during the attack-free period. Material and Methods: The prospective study included 75 familial Mediterranean fever patients during the attack-free period and 50 healthy children. Cardiac evaluation was performed
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Individualised surgical treatment strategy for subaortic stenosis Cardiol. Young (IF 1.0) Pub Date : 2024-04-08 Zhangwei Wang, Kai Ma, Yaobin Zhu, Zhiqiang Li, Shoujun Li
Objectives: The clinical data of patients with subaortic stenosis who underwent surgical treatment in our centre in the past 12 years were reviewed. The short-term and long-term clinical outcomes were analyzed, and the long-term outcomes of different surgical methods for subaortic stenosis were compared to determine the optimal surgical treatment strategy for subaortic stenosis. Methods: From December
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Weight gain in infants with congenital heart disease; breastfeeding alone versus supplemental spoon-feeding of expressed breast milk: an open-label, pilot, randomised control trial. Cardiol. Young (IF 1.0) Pub Date : 2024-04-05 Varsha Jangid, Dinesh Kumar Yadav, Dheeraj Deo Bhatt
Objectives: Infants with congenital heart disease and increased pulmonary blood flow frequently suffer from feeding difficulties and growth failure. Providing expressed breast milk by spoon has been hypothesised to decrease energy expenditure in these infants as compared to breastfeeding. This study assessed the effect of supplemental feeding of expressed breast milk on weight gain in infants with
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Transcatheter recanalisation for absent intra-pericardial pulmonary arteries Cardiol. Young (IF 1.0) Pub Date : 2024-04-05 Amr A. Matoq, Daphney Kernizan, Wolfgang Radtke
Unilateral absence of intra-pericardial pulmonary artery is a rare congenital malformation. If untreated, it can lead to morbidity and mortality in adulthood. Early intervention and restoration of physiologic pulmonary blood flow is necessary. Transcatheter stenting as initial intervention has been rarely reported. We present transcatheter recanalisation and stenting of the obliterated ductus in two
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Relationship between syncopal symptoms and head-up tilt test modes Cardiol. Young (IF 1.0) Pub Date : 2024-04-05 Shuo Wang, Yali Peng, Yuwen Wang, Fang Li, Yi Xu, Huifen Zheng, Heli Yuan, Chunyan Hu, Donglei Liao, Hong Cai, Juan Zhang, Wen Li, Yiyi Ding, Wenhua Zhang, Xiaohong Xue, Xiaoyan Liu, Liping Zhu, Deyu Liu, Meihua Kang, Liping Liu, Weihong Chu, Xiaoming Li, Xuemei Luo, Runmei Zou, Cheng Wang
Objective: Head-up tilt test (HUTT) is an important tool in the diagnosis of pediatric vasovagal syncope. This research will explore the relationship between syncopal symptoms and HUTT modes in pediatric vasovagal syncope. Methods: A retrospective analysis was performed on the clinical data of 2513 children aged 3–18 years, who were diagnosed with vasovagal syncope, from Jan. 2001 to Dec. 2021 due
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Impact of electrophysiologists at daily multidisciplinary report in a paediatric cardiac care unit Cardiol. Young (IF 1.0) Pub Date : 2024-04-05 Matthew F. Mikulski, Andrew Well, Daniel Shmorhun, Carlos M. Mery, Arnold L. Fenrich, Charles D. Fraser
Background: Paediatric cardiac electrophysiologists are essential in CHD inpatient care, but their involvement is typically limited to consultation with individual patients. In our integrated heart centre, an electrophysiologist reviews all cardiac inpatient telemetry over the preceding 24 hours and participates in daily multidisciplinary morning report. This study investigates the impact of the strategy
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Efficacy of catheter ablation in ganglionated plexus for malignant vasovagal syncope children Cardiol. Young (IF 1.0) Pub Date : 2024-04-04 Hongxia Li, Wei Shao, Xia Yu, Lu Gao, Yue Yuan
Aim: Malignant vasovagal syncope in children seriously affects their physical and mental health. Our study aimed to explore the efficacy of catheter ablation in ganglionated plexus with malignant vasovagal syncope children. Conclusion: Catheter ablation of ganglionated plexus was safe and effective in children with malignant vasovagal syncope and can be used as a treatment option for these children
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Invasive haemodynamics predict outcomes in paediatric pulmonary artery hypertension Cardiol. Young (IF 1.0) Pub Date : 2024-04-04 Rupesh Kumar Natarajan, Nathan Rodgers, Shanti Narasimhan, Matthew Ambrose, Abraham Rothman, Michael Shyne, Michael Evans, Varun Aggarwal
Background: Invasive haemodynamics are often performed for initiating and guiding pulmonary artery hypertension therapy. Little is known about the predictive value of invasive haemodynamic indices for long-term outcomes in children with pulmonary artery hypertension. We aimed to evaluate invasive haemodynamic data to help predict outcomes in paediatric pulmonary artery hypertension. Methods: Patients
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Atrioventricular valve surgery in patients with univentricular heart and two separate atrioventricular valves Cardiol. Young (IF 1.0) Pub Date : 2024-04-03 Benedikt Mayr, Takuya Osawa, Helena Staehler, Thibault Schaeffer, Christoph Röhlig, Julie Cleuziou, Alfred Hager, Peter Ewert, Jürgen Hörer, Rüdiger Lange, Masamichi Ono
Objectives: Atrioventricular valve regurgitation in patients with univentricular heart is a well-known risk factor for adverse outcomes and atrioventricular valve repair remains a particular surgical challenge. Methods: We reviewed all surgical atrioventricular valve procedures in patients with univentricular heart and two separate atrioventricular valves who underwent surgical palliation. Endpoints
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Giant aortic aneurysm repair in a child due to arterial tortuosity syndrome Cardiol. Young (IF 1.0) Pub Date : 2024-04-01 Dominykas Budrys, Virgilijus Tarutis, Karolis Jonas
Arterial tortuosity syndrome is an extremely rare hereditary connective tissue disorder. We present a case of an incidentally diagnosed aneurysm of the aortic root and the ascending aorta caused by arterial tortuosity syndrome, which was confirmed genetically. The aneurysm was repaired surgically. One year after the procedure, there was no further dilation of the aorta or formation of new aneurysms
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Immunisation deferral practices surrounding congenital heart surgery Cardiol. Young (IF 1.0) Pub Date : 2024-04-01 Dana B. Gal, John D. Cleveland, Jeffrey E. Vergales, Alaina K. Kipps
Background: Perioperative immunisation administration surrounding congenital heart surgery is controversial. Delayed immunisation administration results in children being at risk of vaccine-preventable illnesses and is associated with failure to complete immunisation schedules. Among children with CHD, many of whom are medically fragile, vaccine-preventable illnesses can be devastating. Limited research
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Bicuspidisation of unicuspid stenotic pulmonary valve in a nine-year-old male Cardiol. Young (IF 1.0) Pub Date : 2024-03-26 Florin Anghel, Catalin Constantin Badiu, Alain J. Poncelet
We report the case of a 9-year-old male with severe congenital pulmonary valve stenosis referred to our centre for percutaneous valvotomy. On admission, trans-thoracic echocardiogram confirmed a unicuspid pulmonary valve with a peak/mean pulmonary valve gradient of 91/53 mmHg and a pulmonary annulus of 13.8 mm (−0.8 Z Score). It also showed an enlarged RV (RV/LV ratio 0,9). During cardiac catheterisation
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NT-proBNP cardiac value in COVID-19: a focus on the paediatric population Cardiol. Young (IF 1.0) Pub Date : 2024-03-26 Bshara Sleem, Christophe El Rassi, Rana Zareef, Fadi Bitar, Mariam Arabi
NT-proBNP is a peptide related to brain natriuretic peptide, a cardiac biomarker and a member of the natriuretic family of peptides. NT-proBNP has demonstrated its clinical utility in the assessment of a wide spectrum of cardiac manifestations. It is also considered a more precise diagnostic and prognostic cardiac biomarker than brain natriuretic peptide. With the appearance of the Severe Acute Respiratory
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Effects of transition programmes to adulthood for adolescents and young adults with CHD: a systematic review with meta-analysis Cardiol. Young (IF 1.0) Pub Date : 2024-03-25 Bo Ryeong Lee, Hyun Young Koo, Sangmi Lee
Background: The increased survival rate among individuals with CHD has sparked interest in their transition to adult healthcare. Although there is a general agreement on the importance of transition interventions, the empirical evidence supporting them is insufficient. Therefore, this study aimed to conduct a systematic review and meta-analysis of transition interventions for adult healthcare in adolescents
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Detection of occult thrombosis in individuals with Fontan circulation by cardiac MRI Cardiol. Young (IF 1.0) Pub Date : 2024-03-20 Samantha F. Curtis, Mariah Cicioni, Alexandria Mullikin, Jason Williams, J. Michael Campbell, Piers C. A. Barker, Andrew W. McCrary
Objective: Identifying thrombus formation in Fontan circulation has been highly variable, with reports between 17 and 33%. Initially, thrombus detection was mainly done through echocardiograms. Delayed-enhancement cardiac MRI is emerging as a more effective imaging technique for thrombus identification. This study aims to determine the prevalence of occult cardiac thrombosis in patients undergoing
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Modified Senning procedure in a patient with dextrocardia with left atrial isomerism and anomalous systemic venous drainage: a rare case report Cardiol. Young (IF 1.0) Pub Date : 2024-03-20 Sayar Kumar Munshi, Caroline Jones, Ramana Dhannapuneni
The atrial switch procedure by Senning or Mustard technique primarily aims in correcting parallel systemic and pulmonary circulations at atrial level. This procedure may be used in late presenting D-transposition of great arteries with a deconditioned left ventricle, congenitally corrected transposition of great arteries and isolated ventricular inversion. We describe the case of a child with dextrocardia
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Prospective evaluation of acute neurological events after paediatric cardiac surgery Cardiol. Young (IF 1.0) Pub Date : 2024-03-14 Olivia Frost, Deborah Ridout, Warren Rodrigues, Paul Wellman, Jane Cassidy, Victor T. Tsang, Dan Dorobantu, Serban C. Stoica, Aparna Hoskote, Katherine L. Brown
Objectives: Children with CHD are at heightened risk of neurodevelopmental problems; however, the contribution of acute neurological events specifically linked to the perioperative period is unclear. Aims: This secondary analysis aimed to quantify the incidence of acute neurological events in a UK paediatric cardiac surgery population, identify risk factors, and assess how acute neurological events
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Successful ductal stent implantation for initial palliation in two patients with aortic atresia and interrupted aortic arch Cardiol. Young (IF 1.0) Pub Date : 2024-03-13 Ensar Duras, Hacer Kamali, Selman Gokalp, Aysel Turkvatan, Alper Guzeltas
The coexistence of aortic valve atresia and interrupted aortic arch are an extremely rare condition. In this pathology, blood flow to the ascending aorta and coronary arteries should be provided through the ductus arteriosus or collaterals originating from the descending aorta. In rare cases where bilateral ductus arteriosus is present, they can provide circulation. Here, we report two cases in which
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Effect of Yangxin Huoxue Jiedu recipe on inflammatory factors and oxidative stress on viral myocarditis in children Cardiol. Young (IF 1.0) Pub Date : 2024-03-12 Hengrui Hao, Meixia Ji, Kuilong Zhou, Yunxia Zhang, Gaoyin Zhang, Lianying Ruan
Objective: This observation purposed to investigate the effect of the Yangxin Huoxue Jiedu formula on children with viral myocarditis and its effect on inflammatory factors and oxidative response. Materials and methods: A total of 121 children with viral myocarditis were randomly divided into two groups, namely the control group (N = 60) and the traditional Chinese medicine group (N = 61). The control
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Estimation of the inferior caval vein saturation using high-fidelity non-invasive haemodynamic values and validation of modelled estimates Cardiol. Young (IF 1.0) Pub Date : 2024-03-12 Rohit S. Loomba, Saul Flores, Juan S. Farias, Enrique G. Villarreal, Alex Constas
Objectives: Monitoring venous saturation allows identification of inadequate systemic oxygen delivery. The aim was to develop a model using non-invasive haemodynamic variables to estimate the inferior caval vein saturation and to determine its prognostic utility. Methods: This is a single-centre, retrospective study. A Bayesian Pearson’s correlation was conducted to model the inferior caval vein saturation
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Electrocardiographic proarrhythmic changes in pregnancy of women with CHD Cardiol. Young (IF 1.0) Pub Date : 2024-03-11 Constance G. Weismann, Frida Wedlund, Thuva Lindblad Ryd, Emma von Wowern, Joanna Hlebowicz
Objectives: Pregnancy-related physiological adaptations result in increased heart rate as well as electrocardiographic changes such as a mean QTc prolongation of 27 ms. Pregnant women with CHD are at increased risk for cardiovascular complications. The aim of this study was to identify risk factors for abnormally prolonged QTc interval—a risk factor for ventricular arrhythmias—in pregnant women with
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The role of lncRNAKCNQ1OT1/miR-301b/Tcf7 axis in cardiac hypertrophy Cardiol. Young (IF 1.0) Pub Date : 2024-03-08 Mingyao E, Feifei Ren, Yanhua Yu, Haiyan Li, Chao Shen
Objective: Cardiac hypertrophy, acting as a pathologic process of chronic hypertension and coronary disease, and its underlying mechanisms still need to be explored. Long non-coding RNA (LncRNA) potassium voltage-gated channel subfamily Q member 1 Transcript 1 (KCNQ1OT1) has been implicated in myocardial infarction. However, its role in cardiac hypertrophy remains reported. Method: To explore the regulated
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Sequence variations in GATA4 and CITED2 gene among patients with cardiac septation defects from Xinjiang, China Cardiol. Young (IF 1.0) Pub Date : 2024-03-08 Renati Imam, Maimaitiaili Aizezi, Fei Yan, Tao Zhu, Weimin Zhang
Studies have shown that genetic factors play an important role in CHD’s development. The mutations in GATA4 and CITED2 genes result in the failure of the heart to develop normally, thereby leading to septal defects. The present study investigated the underlying molecular aetiology of patients with cardiac septation defects from Xinjiang. We investigated variants of the GATA4 and CITED2 gene coding
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Analysis of haemodynamics surrounding blood transfusions after the arterial switch operation: a pilot study utilising real-time telemetry high-frequency data capture Cardiol. Young (IF 1.0) Pub Date : 2024-03-07 Matthew F. Mikulski, Antonio Linero, Daniel Stromberg, Jeremy T. Affolter, Charles D. Fraser, Carlos M. Mery, Richard P. Lion
Background: Packed red blood cell transfusions occur frequently after congenital heart surgery to augment haemodynamics, with limited understanding of efficacy. The goal of this study was to analyse the hemodynamic response to packed red blood cell transfusions in a single cohort, as “proof-of-concept” utilising high-frequency data capture of real-time telemetry monitoring. Methods: Retrospective review
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Care burden and support needs of caregivers of infants and children with CHDs and dysphagia Cardiol. Young (IF 1.0) Pub Date : 2024-03-07 Vivienne Norman, Liesl Zühlke, Brenda Morrow
Dysphagia is common in children with CHDs, resulting in multiple stressors for their caregivers including having a child with a serious medical condition and coping with their child’s feeding needs. However, relatively little is known about caregivers’ perceptions and experiences of the burden of care and support needs for their child with a CHD and dysphagia in low-middle income contexts. This qualitative
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Evaluation of handgrip strength in children with pulmonary hypertension Cardiol. Young (IF 1.0) Pub Date : 2024-03-07 Akif Kavgacı, Serdar Kula, Elif Berber Maraşlı, Murat Zinnuroğlu, Bülent Çelik, Semiha Terlemez, Sedef Tunaoğlu, Deniz Oğuz
Background: Handgrip strength is a crucial indicator of upper extremity muscular strength and is vital for monitoring disorders like cardiac diseases that restrict a patient’s physical activity and result in muscle atrophy. The aim of our study was to evaluate whether muscle strength loss is present in patients with pulmonary hypertension and whether this test can be an alternative to 6-minute walk
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Lower bone strength in young patients with Fontan circulation compared to controls Cardiol. Young (IF 1.0) Pub Date : 2024-03-07 Anna Wikner, Karna Johansson, Elin Enocson, Magne Sthen Bergdahl, Lena Hansson, Annika Rydberg, Camilla Sandberg
Objectives: Previous reports indicate bone deficits in patients with Fontan circulation. However, the consequences of these deficits on bone strength and when these changes occur are unclear. Aim: To compare the tibial bone strength-strain index between young patients (6–19 years) with Fontan circulation and age- and sex-matched controls, and to determine strength-strain-index in subgroups of children
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Creating a flow restrictor in ductal stenting: a novel technique Cardiol. Young (IF 1.0) Pub Date : 2024-03-06 Tam T. Doan, Yen T. K. Nguyen, T. C. B. Phung
Ductal stenting has transformed the care of neonates with ductal-dependent critical CHD, especially in low-income countries. In small infants, a 3.5- or 4-mm stent may lead to too much pulmonary blood flow resulting in pulmonary oedema. We herein presented a novel technique to restrict ductal stent flow in a premature neonate with pulmonary atresia and intact ventricular septum following radiofrequency